Journal Information
Vol. 11. Issue 5.
Pages 499-504 (September - October 2005)
Share
Share
Download PDF
More article options
Vol. 11. Issue 5.
Pages 499-504 (September - October 2005)
Caso Clínico\Clinical Case
Open Access
Síndroma de Kartagener
Kartagener syndrome
Visits
5017
Kattia Cristina Naves1, João Paulo Vieira dos Santos2, José Henrique Santana3, Gesner Pereira Lopes4
1 Autor. Académica do curso de Medicina da Faculdade de Medicina do Triângulo Mineiro (FMTM), Uberaba-MG.
2 Autor. Acadêmico do curso de Medicina da Faculdade de Medicina do Triângulo Mineiro (FMTM), Uberaba-MG.
3 Colaborador. Chefe do Departamento de Clínica Médica da Faculdade de Medicina do Triângulo Mineiro (FMTM).
4 Colaborador. Chefe do Serviço de Radiologia da Faculdade de Medicina do Triângulo Mineiro (FMTM). Rua Frei Paulino, 30 Bairro Abadia Uberaba - MG
This item has received

Under a Creative Commons license
Article information
Resumo

Apresentouse para atendimento uma mulher de 48 anos, branca, natural e procedente de Uberaba-MG, com quadro de dispneia em repouso, febre, tosse produtiva, escarro esverdeado e dor torácica ventilatório-dependente há 3 dias. Durante a investigação foi visualizada, em radiograma e tomografia de tórax, presença de dextrocardia e consolidação em lobo inferior direito por processo broncopneumónico. Optou-se por internamento e antibioticoterapia. Prosseguiu-se investigação com realização de tomografia de mastóides e cavidades paranasais que indicaram otomastoidite crónica bilateral e imagens de sinusopatia crónica permitindo diagnosticar um caso de síndroma de Kartagener. O nosso objectivo é aduzir novos dados àqueles que pesquisam o assunto para que estejam atentos ao eventual aparecimento desta malformação.

Rev Port Pneumol 2005; XI (5): 499-504

Palavras-chave:
Kartagener
bronquiectasia
situs inversus
dextrocardia
sinusopatia
otomastoidite
Abstract

A White, 48-year-old woman, natural from Uberaba-MG, presented herself to hospital. She had a picture of rest dispnea, fever, productive cough, greenish catarrh and ventilatory-depend-ent thoracic pain, for 3 days. During investigation, through radiogram and thoracic tomography, it was visualized the presence of dextrocardia and consolidation in low right lobe by bron-chopneumonic process. It was opted for hospitalization and antibiotic therapy. Investigation was carried on with tomography of mastoids and paranasal cavities which showed bilateral chronic otomastoiditis and images of chronic sinusopathty allowing the diagnosis of a case of Kartagener Syndrome. Our purpose in this case report is to include new informations for who search about this syndrome.

Rev Port Pneumol 2005; XI (5): 499-504

Key-words:
Kartagener
bronchiectasia
situs inversus,dextrocardia
sinusopathy
ostomastoiditis
Full text is only aviable in PDF
Bibliografia
[1.]
M. Kartagener.
Zur pathogenese der bronchiektasen bei situs viscerum inversus.
Beitr Klin Tuberk, 83 (1933), pp. 489-501
[2.]
A.R. Netto, S.R.B. Cruz, N. Bethlem.
Pneumologia, 4.ª ed, pp. 840-841
[3.]
M. Greenstone, P.J. Cole.
Primary ciliary dyskinesia.
Arch Dis Child, 59 (1984), pp. 704-706
[4.]
R.T. Waiter, J.R. Danielson, H.M. Reyes.
Characterization of a chemotactic defect in patients with Kartagener syndrome.
Arch Otolaryngol Head Neck Surg, 116 (1990), pp. 465-469
[5.]
A.K. Siewert.
Ueber einen Fall von bronchiektasien bein einem: Patienten mit situs inversus viscerum.
Berlin Munchen Tieraerztl Wschr, 2 (1904), pp. 139-141
[6.]
P. Camner.
Human tracheobronchial clearance studies.
Arch Environ Health, 22 (1971), pp. 444
[7.]
P. Camner, B. Mossberg, B.A. Afzelius.
Evidence for congenitally nonfunctioning cilia in the tracheobronchial tract in two subjects.
Am Rev Resp Dis, 12 (1975), pp. 807-809
[8.]
B.A. Afzelius.
A human syndrome caused by immotilite cilia.
Science, 193 (1976), pp. 317-319
[9.]
A.F. Barker.
Bronchiectasis.
N Engl J Med, 346 (2002), pp. 1383-1393
[10.]
B.R. Sethi.
Kartagener´s syndrome and its otological manifestations.
J Laryngol Otol, 89 (1975), pp. 183-188
[11.]
R.M. Bolman, W.G. Wolfe.
Bronchiectasis and bron-chopulmonary sequestration.
Surg Clin North Am, 60 (1980), pp. 867-881
[12.]
M. Marchini, G.A. Losa, et al.
Ultrastructural aspects of endometrial surface in Kartagener syndrome.
Fertility and Sterility, 57 (1992), pp. 461-463
[13.]
V.J. Kay, D.S. Irvine.
Successful in-vitro fertilization pregnancy with spermatozoa from a patient with Kartagener’s syndrome.
Human Reproduction, 15 (2000), pp. 135-138
[14.]
L.B. Holmes, J.B. Blennerhasset, K.F. Austen.
A reappraisal of Kartagener syndrome.
Am J Med Sci, 255 (1968), pp. 13-19
[15.]
L.N. Nogueira Filho.
MaiaMG. Kartagener’s syndrome: report of 2 cases.
Arq Bras Cardiol, 25 (1972), pp. 71-79
[16.]
R. Tonet, G. Biguelini, C.R. Zanchettin, F.E. Mugnol, M.A. Girardi, N.A. Golin.
Síndrome de Kartagener.
Ver. Cien. AMECS, 5 (1996), pp. 74-76
[17.]
R.D. Miller, M.B. Divertie.
Kartagener’s syndrome.
Chest, 62 (1972), pp. 130-135
[18.]
L.C.C.C. Silva.
Doenças broncopulmonares obstrutivas e sinusobronquite.
Compêndio de Pneumologia, 2ª edição, pp. 35-36
[19.]
Eg Miranda, S.M. Valadares, et al.
Síndrome de Kartagener – Relato de caso.
J Bras Med, 72 (1997), pp. 31-36
[20.]
M. Inamitsu, T. Arima, et al.
Ciliary ultrastructure in a child with Kartagener’s syndrome: a transmission electron microscopy study using tannic acid staining.
Eur Arch Otorhinolaryngol, 248 (1990), pp. 49-52
[21.]
C. Guichard, M. Haricane, et al.
Axonemal Dynein Intermediate-Chain Gene (DNAI1) Mutations Result in Situs Inversus and Primary Ciliary Dyskinesia (Kartagener Syndrome).
American Journal of Human Genetics, 64 (2001), pp. 1030
Copyright © 2005. Sociedade Portuguesa de Pneumologia/SPP
Pulmonology
Article options
Tools

Are you a health professional able to prescribe or dispense drugs?