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Vol. 14. Issue 4.
Pages 551-559 (July - August 2008)
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Vol. 14. Issue 4.
Pages 551-559 (July - August 2008)
Caso Clínico/Clinical Case
Open Access
Pneumonia eosinofílica crónica idiopática – A propósito de um caso clínico
Idiopathic chronic eosinophilic pneumonia – A clinical case report
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Carla Valente1, Sónia André1, Alexandra Catarino2, Mário Loureiro3, M. Fontes Baganha4
1 Interna Complementar de Pneumologia
2 Assistente Hospitalar de Pneumologia
3 Director do Serviço de Pneumologia dos HUC
4 Director do Departamento de Ciências Pneumológicas e Alergológicas dos HUC
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Resumo

As pneumonias eosinofílicas constituem um grupo heterogéneo de quadros clínicos que podem comprometer unicamente as vias aéreas, o parênquima pulmonar, ou ambos, caracterizado pela presença de eosinofilia alveolar e infiltrados pulmonares, com ou sem evidência de eosinofilia no sangue periférico1.

A pneumonia eosinofílica crónica idiopática (PECI), descrita por Carrington5 em 1969, é uma doença pulmonar eosinofílica rara, de etiologia desconhecida, caracterizada por eosinofilia periférica, infiltrados pulmonares na telerradiografia torácica e excelente resposta à corticoterapia.

A PECI afecta geralmente mulheres de meia idade, sendo os sintomas mais comuns a tosse, a dispneia, a febre e a perda de peso2.

Os autores apresentam um caso de PECI numa mulher jovem, de 21 anos, raça caucasiana, não fumadora e sem antecedentes patológicos relevantes.

Rev Port Pneumol 2008; XIV (4): 551-559

Palavras-chave:
Pneumonia eosinofílica crónica idiopática
corticoterapia
Abstract

The eosinophilic pneumonias are a heterogeneous group of pulmonary disorders, which may compromise only the air ways, the pulmonary parenchyma, or both, characterised by alveolar eosinophils and infiltration of pulmonary tissue, with or without peripheral blood eosinophilia1.

Idiopathic Chronic Eosinophilic Pneumonia (ICEP), detailed description was by Carrington5 in 1969, is a rare eosinophilic lung disease, of unknown aetiology, characterised by peripheral blood eosinophilia, chest radiograph infiltrates and prompt response to corticosteroid therapy.

ICEP most commonly affects women of middle age and usual symptoms are cough, dyspnea, fever and weight loss2.

The authors present a case of ICEP in a young woman, 21 years old, non-smoker and previously healthy.

Rev Port Pneumol 2008; XIV (4): 551-559

Key-words:
Idiopathic chronic eosinophilic pneumonia
corticosteroid therapy
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Bibliografia
[1.]
J.P.F. Batista, P.C. Casanova, J.P.A. Sousa, P.J. Martins, A. Simões, V. Fernandes, J. Souto, J.J. Costa, A. Rebelo, L. Carvalho, J. Pimentel.
Pneumonia eosinofílica aguda com evolução para síndroma de dificuldade respiratória aguda – caso clínico.
Rev Port Pneumol, X (2004), pp. 355-364
[2.]
Y.S. Samman, S.O. Wali, M.A. Abdelaal, M.T. Gangi, A.B. Krayem.
Chronic Eosinophilic Pneumonia Presenting Effusion – Case Report.
Chest, 119 (2001), pp. 968-970
[3.]
E. Magalhães, B. Tavares, C. Chieira.
Pneumonias eosinofílicas – artigo de revisão.
Rev Port Imunol, 14 (2006), pp. 196-217
[4.]
A.I. Zille, C. Perin, G.R. Geyer, J.L. Hetzel, A.S. Rubin.
Pneumonia eosinofílica crónica – caso clínico.
J Pneumol, 28 (2002), pp. 281-284
[5.]
C.B. Carrington, W.W. Addington, A.M. Goff, I.M. Madoff, A. Marks, J.R. Schwaber, et al.
Chronic eosinophilic pneumonia.
N Engl J Med, 280 (1969), pp. 787-798
[6.]
E. Marchand, M. Reynaud-Gaubert, D. Lauque, J. Durieu, A.B. Tonnel, J.F. Cordier.
Idiopathic chronic eosinophilic pneumonia. A clinical and follow-up study of 62 cases.
Medicine Baltimore, 77 (1998), pp. 299-312
[7.]
Y.S. Samman, S.O. Wali, M.A. Abdelaal, M.T. Gangi, A.B. Krayem.
Chronic eosinophilic pneumonia presenting with recurrent massive bilateral pleural effusion.
Chest, 119 (2001), pp. 968-970
[8.]
C. Kroegel, A. Reissig, B. Mock.
Eosinophilic pneumonia.
Respiratory Medicine, 3rd ed., pp. 1643-1659
[9.]
V. Cottin, J.F. Cordier.
Eosinophilic pneumonias.
[10.]
J.N. Allen, W.B. Davis.
Eosinophilic lung diseases.
Am J Respir Crit Care. Med, 150 (1994), pp. 1423-1438
[11.]
H. Matsuse, T. Shimoda, C. Fukushima.
Diagnostic problems in chronic eosinophilic pneumonia.
J Int Med Res, 25 (1997), pp. 196-201
[12.]
J.S. Vourlekis.
Eosinophilic pneumonias.
pp. 167-172
[13.]
E. Marchand, J.F. Cordier.
Idiopathic chronic eosinophilic pneumonia.
Orphaned Encyclopedia, (2004),
[14.]
E.A. Gaensler, C.B. Carrington.
Peripheral opacities in chronic eosinophilic pneumonia:the photographic negative of pulmonary edema.
[15.]
L.T. Tanoue.
The eosinophilic pneumonias.
3rd ed, pp. 408-422
[16.]
C.L. Rochester.
The eosinophilic pneumonias.
Pulmonary diseases and disorders, 3rd ed, pp. 1134-1140
[17.]
M. Naughton, J. Fahy, M.X. FitzGerald.
Chronic eosinophilic pneumonia. A long-term follow-up of 12 patients.
Chest, 103 (1993), pp. 162-165
[18.]
A. Mahmood, N.K. Burki.
Inhaled corticosteroids in the treatment of chronic eosinophilic pneumonia.
Chest, 116 (1999), pp. 426-427
Copyright © 2008. Sociedade Portuguesa de Pneumologia/SPP
Pulmonology
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